Per Westermark

The question of strains in AA amyloidosis

Westermark, Gunilla; Nyström, Ebba; Nyström, Sofie; Nilsson, K. Peter R. et al.

Part of Scientific Reports, 2025

• DOI for The question of strains in AA amyloidosis
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Amyloid nomenclature 2024: update, novel proteins, and recommendations by the International Society of Amyloidosis (ISA) Nomenclature Committee

Buxbaum, Joel N.; Eisenberg, David S.; Fändrich, Marcus; McPhail, Ellen D. et al.

Part of Amyloid, p. 249-256, 2024

• DOI for Amyloid nomenclature 2024: update, novel proteins, and recommendations by the International Society of Amyloidosis (ISA) Nomenclature Committee

Changes in the amyloid editorial board members and in editor positions

Schönland, Stefan; Westermark, Per

Part of Amyloid, p. 85-85, 2024

• DOI for Changes in the amyloid editorial board members and in editor positions

Successes in translation

Westermark, Per; Merlini, Giampaolo

Part of Amyloid, p. 159-167, 2024

• DOI for Successes in translation
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Regionalization of cell types in silk glands of Larinioides sclopetarius suggest that spider silk fibers are complex layered structures

Sonavane, Sumalata; Westermark, Per; Rising, Anna; Holm, Lena

Part of Scientific Reports, 2023

• DOI for Regionalization of cell types in silk glands of Larinioides sclopetarius suggest that spider silk fibers are complex layered structures
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The question of strains in AA amyloidosis

Westermark, Gunilla; Nyström, Ebba; Nyström, Sofie; Nilsson, K. Peter R. et al.

Part of Scientific Reports, 2025

• DOI for The question of strains in AA amyloidosis
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Amyloid nomenclature 2024: update, novel proteins, and recommendations by the International Society of Amyloidosis (ISA) Nomenclature Committee

Buxbaum, Joel N.; Eisenberg, David S.; Fändrich, Marcus; McPhail, Ellen D. et al.

Part of Amyloid, p. 249-256, 2024

• DOI for Amyloid nomenclature 2024: update, novel proteins, and recommendations by the International Society of Amyloidosis (ISA) Nomenclature Committee

Changes in the amyloid editorial board members and in editor positions

Schönland, Stefan; Westermark, Per

Part of Amyloid, p. 85-85, 2024

• DOI for Changes in the amyloid editorial board members and in editor positions

Regionalization of cell types in silk glands of Larinioides sclopetarius suggest that spider silk fibers are complex layered structures

Sonavane, Sumalata; Westermark, Per; Rising, Anna; Holm, Lena

Part of Scientific Reports, 2023

• DOI for Regionalization of cell types in silk glands of Larinioides sclopetarius suggest that spider silk fibers are complex layered structures
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The effect of high-dose vitamin D supplementation on hepcidin-25 and erythropoiesis in patients with chronic kidney disease

Pistis, Kristin Danielson; Westermark, Per; Qureshi, Abdul Rashid; Beshara, Soheir et al.

Part of BMC Nephrology, 2023

• DOI for The effect of high-dose vitamin D supplementation on hepcidin-25 and erythropoiesis in patients with chronic kidney disease
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Amyloid nomenclature 2022: update, novel proteins, and recommendations by the International Society of Amyloidosis (ISA) Nomenclature Committee

Buxbaum, Joel N.; Dispenzieri, Angela; Eisenberg, David S.; Fändrich, Marcus et al.

Part of Amyloid, p. 213-219, 2022

• DOI for Amyloid nomenclature 2022: update, novel proteins, and recommendations by the International Society of Amyloidosis (ISA) Nomenclature Committee

Tissue biopsy for the diagnosis of amyloidosis: experience from some centres

Benson, Merrill D.; Berk, John L.; Dispenzieri, Angela; Damy, Thibaud et al.

Part of Amyloid, p. 8-13, 2022

• DOI for Tissue biopsy for the diagnosis of amyloidosis: experience from some centres
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Tissue-based diagnosis of systemic amyloidosis: Experience of the informal diagnostic center at Uppsala University Hospital

Vesterlund Damjanovic, Justina; Ihse, Elisabet; Thelander, Ulrika; Zancanaro, Alice et al.

Part of Upsala Journal of Medical Sciences, 2022

• DOI for Tissue-based diagnosis of systemic amyloidosis: Experience of the informal diagnostic center at Uppsala University Hospital
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AA amyloid in human food chain is a possible biohazard

Rising, Anna; Gherardi, Paola; Chen, Gefei; Johansson, Jan et al.

Part of Scientific Reports, 2021

• DOI for AA amyloid in human food chain is a possible biohazard
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Clarification on the definition of complete haematologic response in light-chain (AL) amyloidosis

Palladini, Giovanni; Schoenland, Stefan O.; Sanchorawala, Vaishali; Kumar, Shaji et al.

Part of Amyloid, p. 1-2, 2021

• DOI for Clarification on the definition of complete haematologic response in light-chain (AL) amyloidosis

Clinical ApoA-IV amyloid is associated with fibrillogenic signal sequence

Canetti, Diana; Nocerino, Paola; Rendell, Nigel B.; Botcher, Nicola et al.

Part of Journal of Pathology, p. 311-318, 2021

• DOI for Clinical ApoA-IV amyloid is associated with fibrillogenic signal sequence

Transthyretin amyloid deposits in lumbar spinal stenosis and assessment of signs of systemic amyloidosis

Eldhagen, P.; Berg, S.; Lund, L. H.; Sorensson, P. et al.

Part of Journal of Internal Medicine, p. 895-905, 2021

• DOI for Transthyretin amyloid deposits in lumbar spinal stenosis and assessment of signs of systemic amyloidosis
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Amyloid nomenclature 2020: update and recommendations by the International Society of Amyloidosis (ISA) nomenclature committee

Benson, Merrill D.; Buxbaum, Joel N.; Eisenberg, David S.; Merlini, Giampaolo et al.

Part of Amyloid, p. 217-222, 2020

• DOI for Amyloid nomenclature 2020: update and recommendations by the International Society of Amyloidosis (ISA) nomenclature committee
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Subkutant injicerat insulin kan ge amyloidinlagring: Diagnostiska dilemman och fallgropar för patologen och oanade konsekvenser för diabetologen: [Amyloid from insulin treatment: a pitfall for the pathologist and the diabetologist]

Espes, Daniel; Westermark, Per

Part of Läkartidningen, 2020

Abdominal fat pad biopsies exhibit good diagnostic accuracy in patients with suspected transthyretin amyloidosis

Rokke, Hedvig Paulsson; Gousheh, Nima Sadat; Westermark, Per; Suhr, Ole B. et al.

Part of Orphanet Journal of Rare Diseases, 2020

• DOI for Abdominal fat pad biopsies exhibit good diagnostic accuracy in patients with suspected transthyretin amyloidosis
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Experimental transmission of AA amyloidosis in the European brown hare (Lepus europaeus) - first results

Posautz, Annika; Westermark, Per

Part of Amyloid, p. 121-122, 2019

• DOI for Experimental transmission of AA amyloidosis in the European brown hare (Lepus europaeus) - first results

Transthyretin Glu54Leu-an unknown mutation within the Swedish population associated with amyloid cardiomyopathy and a unique fibril type

Hellman, Urban; Lang, Kenneth; Ihse, Elisabet; Jonasson, Jenni et al.

Part of Scandinavian Journal of Clinical and Laboratory Investigation, p. 372-376, 2019

• DOI for Transthyretin Glu54Leu-an unknown mutation within the Swedish population associated with amyloid cardiomyopathy and a unique fibril type
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Robert Kisilevsky, MD, PhD, 1937–2019

Bellotti, Vittorio; Merlini, Giampaolo; Westermark, Per

Part of Amyloid, p. 179-179, 2019

• DOI for Robert Kisilevsky, MD, PhD, 1937–2019

Cryo-EM structure of a transthyretin-derived amyloid fibril from a patient with hereditary ATTR amyloidosis

Schmidt, Matthias; Wiese, Sebastian; Adak, Volkan; Engler, Jonas et al.

Part of Nature Communications, 2019

• DOI for Cryo-EM structure of a transthyretin-derived amyloid fibril from a patient with hereditary ATTR amyloidosis
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Cryo-EM fibril structures from systemic AA amyloidosis reveal the species complementarity of pathological amyloids

Liberta, Falk; Loerch, Sarah; Rennegarbege, Matthies; Schierhorn, Angelika et al.

Part of Nature Communications, 2019

• DOI for Cryo-EM fibril structures from systemic AA amyloidosis reveal the species complementarity of pathological amyloids
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Amyloid fibril composition within hereditary Val30Met (p. Val50Met) transthyretin amyloidosis families

Suhr, Ole Bernt; Wixner, Jonas; Anan, Intissar; Lundgren, Hans-Erik et al.

Part of PLOS ONE, 2019

• DOI for Amyloid fibril composition within hereditary Val30Met (p. Val50Met) transthyretin amyloidosis families
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A case report of osteoarthritis associated with hereditary transthyretin amyloidosis ATTRV30M

Anan, Intissar; Bång, Joakim; Lundgren, Hans-Erik; Wixner, Jonas et al.

Part of Amyloid, p. 29-30, 2019

• DOI for A case report of osteoarthritis associated with hereditary transthyretin amyloidosis ATTRV30M

Is there a connection between the microbiome and AA amyloidosis?: First hints from the European brown hare (Lepus europaeus)

Posautz, Annika; Loncaric, Igor; Westermark, Per

Part of Amyloid, p. 119-120, 2019

• DOI for Is there a connection between the microbiome and AA amyloidosis?: First hints from the European brown hare (Lepus europaeus)

The Swedish open-label diflunisal trial (DFNS01) on hereditary transthyretin amyloidosis and the impact of amyloid fibril composition

Wixner, Jonas; Westermark, Per; Ihse, Elisabet; Pilebro, Björn et al.

Part of Amyloid, p. 39-40, 2019

• DOI for The Swedish open-label diflunisal trial (DFNS01) on hereditary transthyretin amyloidosis and the impact of amyloid fibril composition
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Reduced left atrial myocardial deformation irrespective of cavity size: a potential cause for atrial arrhythmia in hereditary transthyretin amyloidosis

Henein, Michael Y.; Suhr, Ole B.; Arvidsson, Sandra; Pilebro, Björn et al.

Part of Amyloid, p. 46-53, 2018

• DOI for Reduced left atrial myocardial deformation irrespective of cavity size: a potential cause for atrial arrhythmia in hereditary transthyretin amyloidosis
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Alan S. Cohen 1926-2018

Skinner, Martha; Westermark, Per

Part of Amyloid, p. 213-214, 2018

• DOI for Alan S. Cohen 1926-2018

Noncerebral Amyloidoses: Aspects on Seeding, Cross-Seeding, and Transmission

Westermark, Gunilla; Faendrich, Marcus; Lundmark, Katarzyna; Westermark, Per

Part of Cold Spring Harbor Perspectives in Medicine, 2018

• DOI for Noncerebral Amyloidoses: Aspects on Seeding, Cross-Seeding, and Transmission

Post mortem findings and their relation to AA amyloidosis in free-ranging Herring gulls (Larus argentatus)

Jansson, Desiree S.; Bröjer, Caroline; Neimanis, Aleksija; Mörner, Torsten et al.

Part of PLOS ONE, 2018

• DOI for Post mortem findings and their relation to AA amyloidosis in free-ranging Herring gulls (Larus argentatus)

Development of Mouse Monoclonal Antibodies Against Human Amyloid Fibril Proteins for Diagnostic and Research Purposes

Westermark, Gunilla T; Ihse, Elisabet; Westermark, Per

Part of Methods in Molecular Biology, p. 401-414, 2018

• DOI for Development of Mouse Monoclonal Antibodies Against Human Amyloid Fibril Proteins for Diagnostic and Research Purposes

Amyloid nomenclature 2018: recommendations by the International Society of Amyloidosis (ISA) nomenclature committee

Benson, Merrill D.; Buxbaum, Joel N.; Eisenberg, David S.; Merlini, Giampaolo et al.

Part of Amyloid, p. 215-219, 2018

• DOI for Amyloid nomenclature 2018: recommendations by the International Society of Amyloidosis (ISA) nomenclature committee
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Positron emission tomography (PET) utilizing Pittsburgh compound B (PIB) for detection of amyloid heart deposits in hereditary transthyretin amyloidosis (ATTR)

Pilebro, Björn; Arvidsson, Sandra; Lindqvist, Per; Sundström, Torbjörn et al.

Part of Journal of Nuclear Cardiology, p. 240-248, 2018

• DOI for Positron emission tomography (PET) utilizing Pittsburgh compound B (PIB) for detection of amyloid heart deposits in hereditary transthyretin amyloidosis (ATTR)
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Different population - different prevalence or, what is going on in the European brown hare (Lepus europaeus)

Posautz, Annika; Kuebber-Heiss, Anna; Westermark, Per

Part of Amyloid, p. 142-143, 2017

• DOI for Different population - different prevalence or, what is going on in the European brown hare (Lepus europaeus)

Systemic AA amyloidosis in the red fox (Vulpes vulpes)

Rising, Anna; Cederlund, Ella; Palmberg, Carina; Uhlhorn, Henrik et al.

Part of Protein Science, p. 2312-2318, 2017

• DOI for Systemic AA amyloidosis in the red fox (Vulpes vulpes)

Domino liver transplantation: full-length transthyretin in donor and recipient patients with ATTR Val30Met amyloidosis

Westermark, Per; Nowak, Greg; Suhr, Ole B.; Ericzon, Bo-Goran

Part of Amyloid, p. 128-129, 2017

• DOI for Domino liver transplantation: full-length transthyretin in donor and recipient patients with ATTR Val30Met amyloidosis

The challenging histological diagnosis of transthyretin (ATTR) amyloidosis

Charkhkar, Ellahe; Westermark, Per

Part of Amyloid, p. 130-131, 2017

• DOI for The challenging histological diagnosis of transthyretin (ATTR) amyloidosis

Seed-dependent templating of murine AA amyloidosis

Nyström, Sofie; Panahi, Aida Vahdat Shariat; Nilsson, K. Peter R.; Westermark, Per et al.

Part of Amyloid, p. 140-141, 2017

• DOI for Seed-dependent templating of murine AA amyloidosis

C-11 and F-18 Radiolabeling of Tetra- and Pentathiophenes as PET-Ligands for Amyloid Protein Aggregates

Nordeman, Patrik; Johansson, Leif B. G.; Back, Marcus; Estrada, Sergio et al.

Part of ACS Medicinal Chemistry Letters, p. 368-373, 2016

• DOI for C-11 and F-18 Radiolabeling of Tetra- and Pentathiophenes as PET-Ligands for Amyloid Protein Aggregates

Substoichiometric inhibition of transthyretin misfolding by immune-targeting sparsely populated misfolding intermediates: a potential diagnostic and therapeutic for TTR amyloidoses

Galant, Natalie J.; Bugyei-Twum, Antoinette; Rakhit, Rishi; Walsh, Patrick et al.

Part of Scientific Reports, 2016

• DOI for Substoichiometric inhibition of transthyretin misfolding by immune-targeting sparsely populated misfolding intermediates: a potential diagnostic and therapeutic for TTR amyloidoses
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Electron tomography reveals the fibril structure and lipid interactions in amyloid deposits

Kollmer, Marius; Meinhardt, Katrin; Haupt, Christian; Liberta, Falk et al.

Part of Proceedings of the National Academy of Sciences of the United States of America, p. 5604-5609, 2016

• DOI for Electron tomography reveals the fibril structure and lipid interactions in amyloid deposits

Amyloid fibril proteins and amyloidosis: chemical identification and clinical classification International Society of Amyloidosis 2016 Nomenclature Guidelines

Sipe, Jean D.; Benson, Merrill D.; Buxbaum, Joel N.; Ikeda, Shu-ichi et al.

Part of Amyloid, p. 209-213, 2016

• DOI for Amyloid fibril proteins and amyloidosis: chemical identification and clinical classification International Society of Amyloidosis 2016 Nomenclature Guidelines

Establishing the fluorescent amyloid ligand h-FTAA for studying human tissues with systemic and localized amyloid

Sjölander, Daniel; Roecken, Christoph; Westermark, Per; Westermark, Gunilla T. et al.

Part of Amyloid, p. 98-108, 2016

• DOI for Establishing the fluorescent amyloid ligand h-FTAA for studying human tissues with systemic and localized amyloid

Tc-99m-DPD uptake reflects amyloid fibril composition in hereditary transthyretin amyloidosis

Pilebro, Björn; Suhr, Ole B.; Näslund, Ulf; Westermark, Per et al.

Part of Upsala Journal of Medical Sciences, p. 17-24, 2016

• DOI for Tc-99m-DPD uptake reflects amyloid fibril composition in hereditary transthyretin amyloidosis
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Knee osteoarthritis associated with different kinds of amyloid deposits and the impact of aging on type of amyloid

Yanagisawa, Akihiro; Ueda, Mitsuharu; Sueyoshi, Takanao; Nakamura, Eiichi et al.

Part of Amyloid, p. 26-32, 2016

• DOI for Knee osteoarthritis associated with different kinds of amyloid deposits and the impact of aging on type of amyloid

A novel transthyretin Lys70Glu (p.Lys90Glu) mutation presenting with vitreous amyloidosis and carpal tunnel syndrome

Raivio, Virpi Elisa; Jonasson, Jenni; Myllykangas, Liisa; Ala-Mello, Sirpa et al.

Part of Amyloid, p. 46-50, 2016

• DOI for A novel transthyretin Lys70Glu (p.Lys90Glu) mutation presenting with vitreous amyloidosis and carpal tunnel syndrome

Gender related differences in cardiac function in patients with hereditary transthyretin amyloidosis

Gustavsson, S.; Pilebro, B.; Westermark, Per; Lindqvist, P. et al.

Part of European Journal of Heart Failure, p. 64-65, 2015

Clinical and ultrastructural spectrum of diffuse lung disease associated with surfactant protein C mutations

Peca, Donatella; Boldrini, Renata; Johannson, Jan; Shieh, Joseph T. et al.

Part of European Journal of Human Genetics, p. 1033-1041, 2015

• DOI for Clinical and ultrastructural spectrum of diffuse lung disease associated with surfactant protein C mutations

A genealogical and clinical study of the phenotypical variation within the Swedish transthyretin His88Arg (p. His108Arg) amyloidosis family

Hellman, Urban; Lundgren, Hans-Erik; Westermark, Per; Stafberg, Christina et al.

Part of European Journal of Medical Genetics, p. 211-215, 2015

• DOI for A genealogical and clinical study of the phenotypical variation within the Swedish transthyretin His88Arg (p. His108Arg) amyloidosis family

Amyloid Cardiomyopathy in Hereditary Transthyretin V30M Amyloidosis - Impact of Sex and Amyloid Fibril Composition

Arvidsson, Sandra; Pilebro, Bjorn; Westermark, Per; Lindqvist, Per et al.

Part of PLOS ONE, 2015

• DOI for Amyloid Cardiomyopathy in Hereditary Transthyretin V30M Amyloidosis - Impact of Sex and Amyloid Fibril Composition
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In Vivo Seeding and Cross-Seeding of Localized Amyloidosis A Molecular Link between Type 2 Diabetes and Alzheimer Disease

Oskarsson, Marie E.; Paulsson, Johan F.; Schultz, Sebastian W.; Ingelsson, Martin et al.

Part of American Journal of Pathology, p. 834-846, 2015

• DOI for In Vivo Seeding and Cross-Seeding of Localized Amyloidosis A Molecular Link between Type 2 Diabetes and Alzheimer Disease

Amyloid deposits derived from transthyretin in the ligamentum flavum as related to lumbar spinal canal stenosis.

Yanagisawa, Akihiro; Ueda, Mitsuharu; Sueyoshi, Takanao; Okada, Tatsuya et al.

Part of Modern Pathology, p. 201-207, 2015

• DOI for Amyloid deposits derived from transthyretin in the ligamentum flavum as related to lumbar spinal canal stenosis.

Lars Grimelius and his silver impregnation method-Commentaries on the paper in Upsala Journal of Medical Sciences with the highest number of citations

Westermark, Per

Part of Upsala Journal of Medical Sciences, p. 113-116, 2015

• DOI for Lars Grimelius and his silver impregnation method-Commentaries on the paper in Upsala Journal of Medical Sciences with the highest number of citations

Eighty years of research on islet amyloidosis in Uppsala

Westermark, Gunilla T.; Oskarsson, Marie; Andersson, Arne; Westermark, Per

Part of Upsala Journal of Medical Sciences, p. 117-123, 2015

• DOI for Eighty years of research on islet amyloidosis in Uppsala

In vitro binding of [H-3]PIB to human amyloid deposits of different types

Hellstrom-Lindahl, Ewa; Westermark, Per; Antoni, Gunnar; Estrada, Sergio

Part of Amyloid, p. 21-27, 2014

• DOI for In vitro binding of [H-3]PIB to human amyloid deposits of different types

Carbonic Anhydrase Generates CO2 and H+ That Drive Spider Silk Formation Via Opposite Effects on the Terminal Domains

Andersson, Marlene; Chen, Gefei; Otikovs, Martins; Landreh, Michael et al.

Part of PLoS biology, 2014

• DOI for Carbonic Anhydrase Generates CO2 and H+ That Drive Spider Silk Formation Via Opposite Effects on the Terminal Domains
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Online Registry for Mutations in Hereditary Amyloidosis Including Nomenclature Recommendations

Rowczenio, Dorota M.; Noor, Islam; Gillmore, Julian D.; Lachmann, Helen J. et al.

Part of Human Mutation, 2014

• DOI for Online Registry for Mutations in Hereditary Amyloidosis Including Nomenclature Recommendations

Nomenclature 2014: Amyloid fibril proteins and clinical classification of the amyloidosis

Sipe, Jean D.; Benson, Merrill D.; Buxbaum, Joel N.; Ikeda, Shu-ichi et al.

Part of Amyloid, p. 221-224, 2014

• DOI for Nomenclature 2014: Amyloid fibril proteins and clinical classification of the amyloidosis

Transthyretin-derived amyloidosis: Probably a common cause of lumbar spinal stenosis

Westermark, Per; Westermark, Gunilla T.; Suhr, Ole B.; Berg, Svante

Part of Upsala Journal of Medical Sciences, p. 223-228, 2014

• DOI for Transthyretin-derived amyloidosis: Probably a common cause of lumbar spinal stenosis

Changes in pathological and biochemical findings of systemic tissue sites in familial amyloid polyneuropathy more than 10 years after liver transplantation

Oshima, Toshinori; Kawahara, Satomi; Ueda, Mitsuharu; Kawakami, Yushi et al.

Part of Journal of Neurology, Neurosurgery and Psychiatry, p. 740-746, 2014

• DOI for Changes in pathological and biochemical findings of systemic tissue sites in familial amyloid polyneuropathy more than 10 years after liver transplantation

Life science applications utilizing radiocarbon tracing

Salehpour, Mehran; Håkansson, Karl; Westermark, Per; Antoni, Gunnar et al.

Part of Radiocarbon, p. 865-873, 2013

• DOI for Life science applications utilizing radiocarbon tracing
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In Vivo Visualization of Amyloid Deposits in the Heart with ¹¹C-PIB and PET

Antoni, Gunnar; Lubberink, Mark; Estrada, Sergio; Axelsson, Jan et al.

Part of Journal of Nuclear Medicine, p. 213-220, 2013

• DOI for In Vivo Visualization of Amyloid Deposits in the Heart with ¹¹C-PIB and PET

C-11 and F-18 radiolabeling of tetra and pentatiophenes as PET-ligands for misfolded protein aggregates

Nordeman, Patrik; Hall, Håkan; Hammarstrom, Per; Nilsson, Peter R. et al.

Part of Journal of labelled compounds & radiopharmaceuticals, 2013

Amyloid fibrils containing fragmented ATTR may be the standard fibril composition in ATTR amyloidosis

Ihse, Elisabet; Rapezzi, Claudio; Merlini, Giampaolo; Benson, Merrill D. et al.

Part of Amyloid, p. 142-150, 2013

• DOI for Amyloid fibrils containing fragmented ATTR may be the standard fibril composition in ATTR amyloidosis

Life science application utilizing radiocarbon tracing

Salehpour, Mehran; Håkansson, Karl; Westermark, Per; Antoni, Gunnar et al.

Part of Radiocarbon, p. 865-873, 2013

• DOI for Life science application utilizing radiocarbon tracing

Further Evidence for Amyloid Deposition in Clinical Pancreatic Islet Grafts

Westermark, Gunilla T.; Davalli, Alberto M.; Secchi, Antonio; Folli, Franco et al.

Part of Transplantation, p. 219-223, 2012

• DOI for Further Evidence for Amyloid Deposition in Clinical Pancreatic Islet Grafts

High-resolution structure of a BRICHOS domain and its implications for anti-amyloid chaperone activity on lung surfactant protein C

Willander, Hanna; Askarieh, Glareh; Landreh, Michael; Westermark, Per et al.

Part of Proceedings of the National Academy of Sciences of the United States of America, p. 2325-2329, 2012

• DOI for High-resolution structure of a BRICHOS domain and its implications for anti-amyloid chaperone activity on lung surfactant protein C

Amyloid Fibril Composition as a Predictor of Development of Cardiomyopathy After Liver Transplantation for Hereditary Transthyretin Amyloidosis

Gustafsson, Sandra; Ihse, Elisabet; Henein, Michael Y.; Westermark, Per et al.

Part of Transplantation, p. 1017-1023, 2012

• DOI for Amyloid Fibril Composition as a Predictor of Development of Cardiomyopathy After Liver Transplantation for Hereditary Transthyretin Amyloidosis

Amyloid fibril protein nomenclature: 2012 recommendations from the Nomenclature Committee of the International Society of Amyloidosis

Sipe, J. D.; Benson, M. D.; Buxbaum, J. N.; Ikeda, S. -I et al.

Part of Amyloid, p. 167-170, 2012

• DOI for Amyloid fibril protein nomenclature: 2012 recommendations from the Nomenclature Committee of the International Society of Amyloidosis

Heparan sulfate/heparin promotes transthyretin fibrillization through selective binding to a basic motif in the protein

Noborn, Fredrik; O'Callaghan, Paul; Hermansson, Erik; Zhang, Xiao et al.

Part of Proceedings of the National Academy of Sciences of the United States of America, p. 5584-5589, 2011

• DOI for Heparan sulfate/heparin promotes transthyretin fibrillization through selective binding to a basic motif in the protein

Amyloid diagnosis, subcutaneous adipose tissue, immunohistochemistry and mass spectrometry

Westermark, Per

Part of Amyloid, p. 175-176, 2011

• DOI for Amyloid diagnosis, subcutaneous adipose tissue, immunohistochemistry and mass spectrometry

Amyloid detection and typing: summary of current practice and recommendations of the consensus group

Picken, M M; Westermark, Per

Part of Amyloid : the international journal of experimental and clinical investigation : the official journal of the International Society of Amyloidosis, p. 48-50, 2011

• DOI for Amyloid detection and typing: summary of current practice and recommendations of the consensus group

What is a good journal?

Westermark, Per

Part of Amyloid, p. 91-91, 2011

• DOI for What is a good journal?

Variation in amount of wild-type transthyretin in different fibril and tissue types in ATTR amyloidosis

Ihse, Elisabet; Suhr, Ole B.; Hellman, Ulf; Westermark, Per

Part of Journal of Molecular Medicine, p. 171-180, 2011

• DOI for Variation in amount of wild-type transthyretin in different fibril and tissue types in ATTR amyloidosis

Signs of cross-seeding: aortic medin amyloid as a trigger for protein AA deposition

Larsson, Annika; Malmström, Susanna; Westermark, Per

Part of Amyloid, p. 229-234, 2011

• DOI for Signs of cross-seeding: aortic medin amyloid as a trigger for protein AA deposition

beta-Cell Loss and beta-Cell Apoptosis in Human Type 2 Diabetes Are Related to Islet Amyloid Deposition

Jurgens, Catherine A.; Toukatly, Mirna N.; Fligner, Corinne L.; Udayasankar, Jayalakshmi et al.

Part of American Journal of Pathology, p. 2632-2640, 2011

• DOI for beta-Cell Loss and beta-Cell Apoptosis in Human Type 2 Diabetes Are Related to Islet Amyloid Deposition

Somatostatin Receptor Subtypes in Human Type 2 Diabetic Islets

Portela-Gomes, Guida M.; Grimelius, Lars; Westermark, Per; Stridsberg, Mats

Part of Pancreas, p. 836-842, 2010

• DOI for Somatostatin Receptor Subtypes in Human Type 2 Diabetic Islets

Autosomal recessive pure hair and nail ectodermal dysplasia linked to chromosome 12p11.1-q14.3 without KRTHB5 gene mutation

Rasool, Mahmood; Nawaz, Sadia; Azhar, Aysha; Wajid, Muhammad et al.

Part of EJD. European journal of dermatology, p. 443-446, 2010

• DOI for Autosomal recessive pure hair and nail ectodermal dysplasia linked to chromosome 12p11.1-q14.3 without KRTHB5 gene mutation

Amyloid fibril protein nomenclature: 2010 recommendations from the nomenclature committee of the International Society of Amyloidosis

Sipe, Jean D.; Benson, Merrill D.; Buxbaum, Joel N.; Ikeda, Shu-ichi et al.

Part of Amyloid, p. 101-104, 2010

• DOI for Amyloid fibril protein nomenclature: 2010 recommendations from the nomenclature committee of the International Society of Amyloidosis

Report of five rare or previously unknown amyloidogenic transthyretin mutations disclosed in Sweden

Suhr, Ole B.; Andersen, Oluf; Aronsson, Thomas; Jonasson, Jenni et al.

Part of Amyloid, p. 208-214, 2009

• DOI for Report of five rare or previously unknown amyloidogenic transthyretin mutations disclosed in Sweden

Amyloidose-Zentren in Europa. Das EURAMY-Projekt: [Amyloid centers in Europe. the EURAMY project]

Westermark, Per

Part of Der Pathologe, p. 124-127, 2009

• DOI for Amyloidose-Zentren in Europa. Das EURAMY-Projekt: [Amyloid centers in Europe. the EURAMY project]

Alkali-degradation of amyloid: an ancient method useful for making monoclonal antibodies against amyloid fibril proteins

Westermark, Gunilla T; Sletten, K; Westermark, Per

Part of Scandinavian Journal of Immunology, p. 535-540, 2009

• DOI for Alkali-degradation of amyloid: an ancient method useful for making monoclonal antibodies against amyloid fibril proteins

Fibrils from designed non-amyloid-related synthetic peptides induce AA-amyloidosis during inflammation in an animal model

Westermark, Per; Lundmark, Katarzyna; Westermark, Gunilla T

Part of PloS one, 2009

• DOI for Fibrils from designed non-amyloid-related synthetic peptides induce AA-amyloidosis during inflammation in an animal model

Fibril protein fragmentation pattern in systemic AL-amyloidosis

Enqvist, Stina; Sletten, Knut; Westermark, Per

Part of Journal of Pathology, p. 473-480, 2009

• DOI for Fibril protein fragmentation pattern in systemic AL-amyloidosis

Proportion between wild-type and mutant protein in truncated compared to full-length ATTR: an analysis on transplanted transthyretin T60A amyloidosis patients

Ihse, Elisabet; Stangou, Arie J.; Heaton, Nigel D.; O'Grady, John et al.

Part of Biochemical and Biophysical Research Communications - BBRC, p. 846-850, 2009

• DOI for Proportion between wild-type and mutant protein in truncated compared to full-length ATTR: an analysis on transplanted transthyretin T60A amyloidosis patients

A father and his son with systemic AL amyloidosis

Enqvist, Stina; Mellqvist, Ulf-Henrik; Mölne, Johan; Sletten, Knut et al.

Part of Haematologica, p. 437-439, 2009

• DOI for A father and his son with systemic AL amyloidosis

Splenic plasma cells can serve as a source of amyloidogenic light chains

Solomon, Alan; Macy, Sallie D.; Wooliver, Craig; Weiss, Deborah T. et al.

Part of Blood, p. 1501-1503, 2009

• DOI for Splenic plasma cells can serve as a source of amyloidogenic light chains

Widespread amyloid deposition in transplanted human pancreatic islets

Westermark, Gunilla T.; Westermark, Per; Berne, Christian; Korsgren, Olle

Part of New England Journal of Medicine, p. 977-979, 2008

• DOI for Widespread amyloid deposition in transplanted human pancreatic islets

Amyloid and Transplanted Islets Reply

Westermark, Gunilla T.; Korsgren, Olle; Westermark, Per

Part of New England Journal of Medicine, p. 2729-2731, 2008

Unreliability of immunohistochemistry for typing amyloid deposits

Solomon, Alan; Murphy, Charles L.; Westermark, Per

Part of Archives of Pathology and Laboratory Medicine, p. 14-14, 2008

Amyloid fibril composition is related to the phenotype of hereditary transthyretin V30M amyloidosis

Ihse, E; Ybo, A; Suhr, Ob; Lindqvist, P et al.

Part of Journal of Pathology, p. 253-61, 2008

• DOI for Amyloid fibril composition is related to the phenotype of hereditary transthyretin V30M amyloidosis

Ichthyosis prematurity syndrome: a well-defined congenital ichthyosis subtype

Bygum, Anette; Westermark, Per; Brandrup, Flemming

Part of The Journal of American Academy of Dermatology, 2008

• DOI for Ichthyosis prematurity syndrome: a well-defined congenital ichthyosis subtype

Transthyretin and amyloid in the islets of Langerhans in type-2 diabetes

Westermark, Gunilla T.; Westermark, Per

Part of Experimental Diabetes Research, p. 429274, 2008

• DOI for Transthyretin and amyloid in the islets of Langerhans in type-2 diabetes

Systemiska amyloidoser - ny behandling gör tidig och exakt diagnos allt viktigare

Westermark, Per

Part of Läkartidningen, p. 1517-1521, 2007

Unwinding fibril formation of medin, the peptide of the most common form of human amyloid.

Larsson, Annika; Söderberg, Linda; Westermark, Gunilla T.; Sletten, Knut et al.

Part of Biochemical and Biophysical Research Communications - BBRC, p. 822-828, 2007

• DOI for Unwinding fibril formation of medin, the peptide of the most common form of human amyloid.

Role of aggregated medin in the pathogenesis of thoracic aortic aneurysm and dissection

Peng, Siwei; Larsson, Annika; Wassberg, Erik; Gerwins, Pär et al.

Part of Laboratory Investigation, p. 1195-1205, 2007

• DOI for Role of aggregated medin in the pathogenesis of thoracic aortic aneurysm and dissection

Amyloidogenic potential of foie gras

Solomon, Alan; Richey, Tina; Murphy, Charles L; Weiss, Deborah T et al.

Part of Proceedings of the National Academy of Sciences of the United States of America, p. 10998-11001, 2007

• DOI for Amyloidogenic potential of foie gras

A primer of amyloid nomenclature

Westermark, Per; Benson, Merrill D.; Buxbaum, Joel N.; Cohen, Alan S. et al.

Part of Amyloid, p. 179-183, 2007

• DOI for A primer of amyloid nomenclature

Germ Line Origin and Somatic Mutations Determine the Target Tissues in Systemic AL-Amyloidosis

Enqvist, Stina; Sletten, Knut; Stevens, Fred J.; Hellman, Ulf et al.

Part of PLoS ONE, 2007

• DOI for Germ Line Origin and Somatic Mutations Determine the Target Tissues in Systemic AL-Amyloidosis

Surface exposed epitopes and structural heterogeneity of in vivo formed transthyretin amyloid fibrils

Bergström, Joakim; Engström, Ulla; Yamashita, Taro; Ando, Yukio et al.

Part of Biochemical and Biophysical Research Communications - BBRC, p. 532-539, 2006

• DOI for Surface exposed epitopes and structural heterogeneity of in vivo formed transthyretin amyloid fibrils

Lactadherin binds to elastin -a starting point for medin amyloid formation?

Larsson, Annika; Peng, Siwei; Persson, Helena; Rosenbloom, Joel et al.

Part of Amyloid, p. 78-85, 2006

• DOI for Lactadherin binds to elastin -a starting point for medin amyloid formation?

Misclassification of amyloidosis is unwarranted.

Solomon, Alan; Murphy, Charles L; Westermark, Per

Part of Blood, 2006

Intracellular amyloid-like deposits contain unprocessed pro-islet amyloid polypeptide (proIAPP) in beta cells of transgenic mice overexpressing the gene for human IAPP and transplanted human islets.

Paulsson, J F; Andersson, A; Westermark, P; Westermark, G T

Part of Diabetologia, p. 1237-46, 2006

Subcutaneous fat tissue for diagnosis and studies of systemic amyloidosis.

Westermark, Per; Davey, Eva; Lindbom, Karolina; Enqvist, Stina

Part of Acta Histochem, p. 209-13, 2006

Immunoaffinity chromatographic and immunoprecipitation methods combined with mass spectrometry for characterization of circulating transthyretin.

Heegaard, Niels H H; Hansen, Morten Z; Sen, Jette W; Christiansen, Michael et al.

Part of J Sep Sci, p. 371-7, 2006

Amyloid contained in the knee joint meniscus is formed from apolipoprotein A-I.

Solomon, Alan; Murphy, Charles L; Kestler, Daniel; Coriu, Daniel et al.

Part of Arthritis Rheum, p. 3545-50, 2006

Senile seminal vesicle amyloid is derived from semenogelin I.

Linke, Reinhold P; Joswig, Reinhild; Murphy, Charles L; Wang, Shuching et al.

Part of Journal of Laboratory and Clinical Medicine, p. 187-93, 2005

Betungande regler för klinisk forskning står inte i proportion till patientnyttan

Vahlquist, Anders; Westermark, Per; Ståhle, Elisabeth; Venge, Per et al.

Part of Läkartidningen, p. 1832-1834, 2005

Betungande regler för klinisk prövning står inte i proportion till patientnyttan

Vahlquist, Anders; Westermark, Per; Ståhle, Elisabeth; Venge, Per et al.

Part of Läkartidningen, p. 1832-1834, 2005

Amyloid deposits in transthyretin derived amyloidosis: Cleaved transthyretin is associated with distinct amyloid morphology

Bergström, Joakim; Gustavsson, Åsa; Hellman, Ulf; Sletten, Knut et al.

Part of The Internet Journal of Pathology, p. 224-232, 2005

• DOI for Amyloid deposits in transthyretin derived amyloidosis: Cleaved transthyretin is associated with distinct amyloid morphology

Medin-amyloid: a recently characterized age-associated arterial amyloid form affects mainly arteries in the upper part of the body

Peng, Siwei; Glennert, Johanna; Westermark, Per

Part of Amyloid, p. 96-102, 2005

• DOI for Medin-amyloid: a recently characterized age-associated arterial amyloid form affects mainly arteries in the upper part of the body

A Swedish family with the rare Phe33Leu transthyretin mutation.

Holmgren, Gasta; Hellman, Urban; Jonasson, Jenni; Lundgren, Hans-Eric et al.

Part of Amyloid, p. 189-92, 2005

Aspects on human amyloid forms and their fibril polypeptides.

Westermark, Per

Part of FEBS J, p. 5942-9, 2005

Is aggregated IAPP a cause of beta-cell failure in transplanted human pancreatic islets?

Westermark, Per; Andersson, Arne; Westermark, Gunilla T

Part of Curr Diab Rep, p. 184-8, 2005

Purification of amyloid protein AA subspecies from amyloid-rich human tissues.

Westermark, Gunilla T; Westermark, Per

Part of Methods Mol Biol, p. 243-54, 2005

Protein fibrils in nature can enhance amyloid protein A amyloidosis in mice: Cross-seeding as a disease mechanism.

Lundmark, Katarzyna; Westermark, Gunilla T; Olsen, Arne; Westermark, Per

Part of Proc Natl Acad Sci U S A, p. 6098-102, 2005

Amyloid: toward terminology clarification. Report from the Nomenclature Committee of the International Society of Amyloidosis.

Westermark, Per; Benson, Merrill D; Buxbaum, Joel N; Cohen, Alan S et al.

Part of Amyloid, p. 1-4, 2005

Two different types of amyloid deposits - apolipoprotein A-IV and transthyretin - in a patient with systemic amyloidosis

Bergström, Joakim; Murphy, Charles L.; Weiss, Deborah T.; Solomon, Alan et al.

Part of Lab. Invest., p. 981-988, 2004

Autosomal recessive congenital ichthyosis in Sweden and Estonia: clinical, genetic and ultrastructural findings in eithty-three patients

Gånemo, Agneta; Pigg, Maritta; Virtanen, Marie; Kukk, Terje et al.

Part of Acta Dermato-Venereologica, p. 24-30, 2003

Islet amyloid polypeptide is expressed in the pancreatic islet parenchyma of the Teleostean fish, Myoxocephalus (Cottus) scorpius

Westermark, Gunilla T.; Falkmer, Sture; Steiner, Donald F.; Chan, Shu J. et al.

Part of Comp. Biochem. Physiol. B, p. 119, 2002

Enhanced in vitro production of amyloid-like fibrils from mutant (S20G) islet amyloid polypeptide

Ma, Z; Westermark, GT; Sakagashira, S; Sanke, T et al.

Part of Amyloid, p. 242, 2001

Successes in translation

Westermark, Per; Merlini, Giampaolo

Part of Amyloid, p. 159-167, 2024

• DOI for Successes in translation
• Download full text (pdf) of Successes in translation

Proteostasis of Islet Amyloid Polypeptide: A Molecular Perspective of Risk Factors and Protective Strategies for Type II Diabetes

Milardi, Danilo; Gazit, Ehud; Radford, Sheena E.; Xu, Yong et al.

Part of Chemical Reviews, p. 1845-1893, 2021

• DOI for Proteostasis of Islet Amyloid Polypeptide: A Molecular Perspective of Risk Factors and Protective Strategies for Type II Diabetes

Transthyretin amyloidosis: an under-recognized neuropathy and cardiomyopathy

Galant, Natalie J.; Westermark, Per; Higaki, Jeffrey N.; Chakrabartty, Avijit

Part of Clinical Science, p. 395-409, 2017

• DOI for Transthyretin amyloidosis: an under-recognized neuropathy and cardiomyopathy

One mutation, two distinct disease variants: unravelling the impact of transthyretin amyloid fibril composition

Suhr, O. B.; Lundgren, E.; Westermark, Per

Part of Journal of Internal Medicine, p. 337-347, 2017

• DOI for One mutation, two distinct disease variants: unravelling the impact of transthyretin amyloid fibril composition

Transmissible amyloid

Tjernberg, L. O.; Rising, A.; Johansson, J.; Jaudzems, K. et al.

Part of Journal of Internal Medicine, p. 153-163, 2016

• DOI for Transmissible amyloid

Islet Amyloid Polypeptide and Diabetes

Westermark, Gunilla T.; Westermark, Per

Part of Current protein and peptide science, p. 330-337, 2013

• DOI for Islet Amyloid Polypeptide and Diabetes

Localized AL amyloidosis: A suicidal neoplasm?

Westermark, Per

Part of Upsala Journal of Medical Sciences, p. 244-250, 2012

• DOI for Localized AL amyloidosis: A suicidal neoplasm?

Islet amyloid polypeptide, islet amyloid, and diabetes mellitus

Westermark, Per; Andersson, Arne; Westermark, Gunilla T.

Part of Physiological Reviews, p. 795-826, 2011

• DOI for Islet amyloid polypeptide, islet amyloid, and diabetes mellitus

Localized amyloids important in diseases outside the brain: lessons from the islets of Langerhans and the thoracic aorta

Westermark, Gunilla T.; Westermark, Per

Part of The FEBS Journal, p. 3918-3929, 2011

• DOI for Localized amyloids important in diseases outside the brain: lessons from the islets of Langerhans and the thoracic aorta

Amyloid in the islets of Langerhans: Thoughts and some historical aspects

Westermark, Per

Part of Upsala Journal of Medical Sciences, p. 81-89, 2011

• DOI for Amyloid in the islets of Langerhans: Thoughts and some historical aspects

Prion-like aggregates: infectious agents in human disease

Westermark, Gunilla T.; Westermark, Per

Part of Trends in Molecular Medicine, p. 501-507, 2010

• DOI for Prion-like aggregates: infectious agents in human disease

Serum amyloid A and protein AA: molecular mechanisms of a transmissible amyloidosis

Westermark, Gunilla T.; Westermark, Per

Part of FEBS Letters, p. 2685-2690, 2009

• DOI for Serum amyloid A and protein AA: molecular mechanisms of a transmissible amyloidosis

Amyloid deposition in transplanted human pancreatic islets: a conceivable cause of their long-term failure

Andersson, Arne; Bohman, Sara; Borg, L. A. Håkan; Paulsson, Johan F. et al.

Part of Experimental diabetes research, p. 562985, 2008

• DOI for Amyloid deposition in transplanted human pancreatic islets: a conceivable cause of their long-term failure

Reflections on amyloidosis in Papua New Guinea

Westermark, Per; Westermark, Gunilla T

Part of Philosophical Transactions of the Royal Society of London. Biological Sciences, p. 3701-3705, 2008

• DOI for Reflections on amyloidosis in Papua New Guinea

AA Amyloidosis: Pathogenesis and Targeted Therapy

Westermark, Gunilla T.; Faendrich, Marcus; Westermark, Per

Part of Annual Review Of Pathology, p. 321-344, ANNUAL REVIEWS, 2015

• DOI for AA Amyloidosis: Pathogenesis and Targeted Therapy